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eRAM

encyclopedia of Rare Disease Annotation for Precision Medicine




Disease vasculitis
Comorbidity C0456909|blindness
Sentences 3
PubMedID- 26558256 Ocular disorders occur often in this syndrome typically in the form of a relapsing-remitting panuveitis and vasculitis and can lead to blindness as one of its most disabling complications if left untreated.
PubMedID- 20729261 In conclusion, irreversible blindness due to retinal vasculitis and/or uveitis is a rare and severe lupus manifestation, particularly associated with disease activity and viral infection.
PubMedID- 22497990 The poor long-term visual prognosis is related to ocular hypertension, cataract and retinal vasculitis with blindness occurring in 25 to 30% of cases in most series at 5 years.

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