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eRAM

encyclopedia of Rare Disease Annotation for Precision Medicine




Disease vasculitis
Comorbidity C0043092|wegener\'s granulomatosis
Sentences 13
PubMedID- 23304608 Culture of bronchoalveolar lavage specimen was negative after a 7-day inoculation and the transbronchial lung biopsy (tblb) showed pulmonary angiitis granulomatosis compatible with wegener's granulomatosis.
PubMedID- 25859349 Anti-neutrophil cytoplasmic antibody (anca)-associated vasculitis includes granulomatosis with polyangiitis (wegener's granulomatosis) and microscopic polyangiitis.
PubMedID- 23480833 Expert opinion: small-vessel anti-neutrophil cytoplasmic antibody (anca)-associated vasculitis, especially granulomatosis with polyangiitis (wegener's granulomatosis) are the most frequent causes of pulmonary vasculitis and typically present as nodules, alveolar infiltrates (haemorrhagic or not), cavities or tracheobronchial stenosis.
PubMedID- 22882216 It was approved by the fda for use in refractory rheumatoid arthritis in 2007, and in april 2011 it was approved for the treatment of anti-neutrophil cytoplasmic antibody-associated vasculitides (including granulomatosis with polyangiitis [wegener's granulomatosis] and microscopic polyangiitis), based on the promising results of the rave trial.
PubMedID- 21147630 According to the american college of rheumatology (acr), classification criteria of the css are: small vessel vasculitis along with wegener's granulomatosis (wg), microscopic polyangiitis (mpa), and idiopathic necrotizing crescentic glomerulonephritis ncgn [3].
PubMedID- 22247758 Evidence is lacking for direct pathogenicity of human anti-proteinase-3 (pr3) antibodies in development of systemic vasculitis and granulomatosis with polyangiitis (gpa, wegener's granulomatosis).
PubMedID- 24198834 Granulomatosis with polyangiitis (gpa, wegener's granulomatosis) is one of the systematic vasculitides involved in various organs such as the upper respiratory tract, the lungs, and the kidneys, characterized pathologically by necrotizing granulomatous inflammation [1, 2].
PubMedID- 22895899 The anti-neutrophil cytoplasmic antibody-associated vasculitides include granulomatosis with polyangiitis (wegener's granulomatosis) and microscopic polyangiitis.
PubMedID- 20695860 Granulomatous vasculitis is classically associated with wegener's granulomatosis, lymphomatoid granulomatosis or churg-strauss syndrome.
PubMedID- 22946144 wegener's granulomatosis is a form of systemic vasculitis of small to medium sized vessels and affects upper respiratory tract, lungs and kidneys along with various organs.
PubMedID- 26018737 Granulomatosis with polyangiitis (wegener's granulomatosis) is one of the idiopathicimmune-mediated small-vessel vasculitides described in humans which are characterised bythe presence of circulating antineutrophil cytoplasmic antibodies.
PubMedID- 24189648 Antineutrophil cytoplasmic autoantibody (anca)-associated diseases are small-vessel vasculitides, encompassing granulomatosis with polyangiitis (formerly wegener's granulomatosis), microscopic polyangiitis and eosinophilic granulomatosis with polyangiitis.
PubMedID- 25332635 vasculitis like granulomatosis with polyangitis (wegener's granulomatosis), churg strauss syndrome and sarcoidosis, which are the second consideration, are ruled out by serological investigations.

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