eRAM
encyclopedia of Rare Disease Annotation for Precision Medicine
| Disease | pulmonary arterial hypertension |
| Comorbidity | C0018799|heart disease |
| Sentences | 54 |
| PubMedID- 21893489 | pulmonary arterial hypertension associated with congenital heart disease (pah-chd) using three different response criteria. |
| PubMedID- 23064558 | Comparison of acute hemodynamic effects of aerosolized iloprost and inhaled nitric oxide in adult congenital heart disease with severe pulmonary arterial hypertension. |
| PubMedID- 26459910 | We validated our methods by quantifying mirna expression profiles in the sera of the patients with pulmonary arterial hypertension associated with congenital heart disease. |
| PubMedID- 25076993 | Saudi guidelines on the diagnosis and treatment of pulmonary hypertension: pulmonary arterial hypertension associated with congenital heart disease. |
| PubMedID- 20549685 | pulmonary arterial hypertension associated with congenital heart disease (apah-chd) (n = 61, 34%) was more common than idiopathic pah (ipah) (n = 36, 20%). |
| PubMedID- 24629043 | Apah-chd: pulmonary arterial hypertension associated with congenital heart disease; apah-ctd: pulmonary arterial hypertension associated with connective tissue disease; ci: confidence interval; hr: hazard ratio; mpap: mean pulmonary arterial pressure; nyha: new york heart association; pah: pulmonary arterial hypertension; pcwp: pulmonary capillary wedge pressure; rhc: right heart catheterization; sd: standard deviation; 6mwd: 6-minute walk distance. |
| PubMedID- 24267300 | pulmonary arterial hypertension associated with congenital heart disease. |
| PubMedID- 26413109 | Despite remarkable advances in cardiac surgery and intervention that have allowed repair of congenital heart defects, pulmonary arterial hypertension (pah) associated with congenital heart disease remains a major problem. |
| PubMedID- 21093377 | A review of the management of pulmonary arterial hypertension associated with congenital heart disease. |
| PubMedID- 24225339 | Assessment of operability of patients with pulmonary arterial hypertension associated with congenital heart disease. |
| PubMedID- 21943933 | Efficacy and safety of bosentan for pulmonary arterial hypertension in adults with congenital heart disease. |
| PubMedID- 20875358 | pulmonary arterial hypertension frequently arises in patients with congenital heart disease. |
| PubMedID- 25787791 | pulmonary arterial hypertension associated with congenital heart disease. |
| PubMedID- 23640439 | Accuracy of doppler echocardiography in the assessment of pulmonary arterial hypertension in patients with congenital heart disease. |
| PubMedID- 24571873 | Background: congenital heart disease with severe pulmonary arterial hypertension (spah), previously thought to have irreversible pulmonary vascular disease (pvd), has been recently successfully corrected using diagnostic treatment and repair strategy by our surgery team. |
| PubMedID- 23720182 | [pulmonary arterial hypertension in patients with congenital heart disease: current issues and health care situation]. |
| PubMedID- 22781765 | [screening study of pulmonary arterial hypertension in patients with congenital heart diseases]. |
| PubMedID- 21763017 | Introduction: pulmonary arterial hypertension (pah) in patients with congenital heart disease (chd) usually has a homogeneous pressure distribution. |
| PubMedID- 25549894 | Eisenmenger's syndrome (es) is the most advanced form of pulmonary arterial hypertension (pah) associated with congenital heart diseases (chd). |
| PubMedID- 21723630 | pulmonary arterial hypertension (pah) associated with congenital heart disease (chd) due to systemic to pulmonary shunting is associated with a high risk of morbidity and mortality. |
| PubMedID- 22340653 | Objective: to explore the incidence of congenital heart disease (chd) complicated with pulmonary arterial hypertension (pah) at an altitude of over 2000 meters above sea level. |
| PubMedID- 25008885 | Objective: to observe the clinical efficacy and safety of sildenafil in the treatment of high altitude heart disease associated with severe pulmonary arterial hypertension (pah) in children. |
| PubMedID- 23351920 | However, its long-term efficacy and safety in patients with pulmonary arterial hypertension (pah) associated with complex congenital heart disease (chd) is unknown. |
| PubMedID- 25604592 | pulmonary arterial hypertension associated with congenital heart disease and eisenmenger syndrome: current practice in pediatrics. |
| PubMedID- 23341836 | The world health organization (who) classification divides ph into five categories: pulmonary arterial hypertension; ph with left heart disease; ph secondary to lung disease and chronic hypoxemia; chronic thromboembolic ph (cteph); and miscellaneous. |
| PubMedID- 23280192 | Objective: the aim of this study is to determine the relationship between the cardiac catheterization findings and pulsed-wave (pw) doppler and doppler tissue imaging (dti) in pulmonary arterial hypertension patients with congenital heart disease with intracardiac shunts. |
| PubMedID- 25847058 | Methods: using micrornas microarray, we profiled the micrornas in the lung specimen from 12 congenital heart disease patients, (6 with pulmonary arterial hypertension and the others without). |
| PubMedID- 20728407 | Endothelin receptor antagonists are an effective long term treatment option in pulmonary arterial hypertension associated with congenital heart disease with or without trisomy 21. |
| PubMedID- 23962785 | Background: eisenmenger syndrome (es) represents the extreme manifestation of pulmonary arterial hypertension in patients with congenital heart disease, associated with significant exercise intolerance and mortality. |
| PubMedID- 19958396 | pulmonary arterial hypertension in adults with congenital heart disease. |
| PubMedID- 23204121 | pulmonary arterial hypertension associated with congenital heart disease. |
| PubMedID- 24081196 | Objectives: the treatment of choice for congenital heart disease (chd) with pulmonary arterial hypertension (pah) is still controversial. |
| PubMedID- 23895034 | The challenge of managing pulmonary arterial hypertension in adults with congenital heart disease. |
| PubMedID- 25224243 | [correlation between endogenous sulfur dioxide and homocysteine in children with pulmonary arterial hypertension associated with congenital heart disease]. |
| PubMedID- 26135803 | Riociguat for pulmonary arterial hypertension associated with congenital heart disease. |
| PubMedID- 24790070 | Objectives: to assess the relationship of c-reactive protein (crp) to clinical outcome and mortality in adults with pulmonary arterial hypertension (pah) associated with congenital heart disease (chd-pah). |
| PubMedID- 24577356 | Right ventricular diastolic performance in children with pulmonary arterial hypertension associated with congenital heart disease: correlation of echocardiographic parameters with invasive reference standards by high-fidelity micromanometer catheter. |
| PubMedID- 24093869 | Value of systolic right ventricular function parameters in children with pulmonary arterial hypertension associated with congenital heart diseases. |
| PubMedID- 23041100 | Efficacy of exercise training in pulmonary arterial hypertension associated with congenital heart disease. |
| PubMedID- 24814894 | Blood biomarkers and their potential role in pulmonary arterial hypertension associated with congenital heart disease. |
| PubMedID- 25620261 | [management of pulmonary arterial hypertension associated with congenital heart disease with specific pulmonary arterial hypertension vasoactive drugs combined with transcatheter closure strategy:a case report]. |
| PubMedID- 24176071 | Uncorrected congenital heart disease (chd) frequently leads to pulmonary arterial hypertension (pah), the most severe form of which is eisenmenger syndrome (es). |
| PubMedID- 25443244 | pulmonary arterial hypertension associated with congenital heart disease: recent advances and future directions. |
| PubMedID- 22068906 | Plasma von willebrand factor as a predictor of survival in pulmonary arterial hypertension associated with congenital heart disease. |
| PubMedID- 25737007 | This study investigated the clinical value of plasma asymmetrical dimethyl-l-arginine (adma) level in the diagnosis, staging, and treatment response in congenital heart disease (chd) patients with pulmonary arterial hypertension (pah). |
| PubMedID- 25362943 | Objectives: eisenmenger syndrome (es) occurs as the most advanced form of pulmonary arterial hypertension (pah) in patients with congenital heart disease. |
| PubMedID- 25650280 | The progressive rise in pulmonary vascular resistance and increased pressures in the right heart provocated reversal of the shunt may arise with the development of eisenmenger' syndrome the most advanced form de pulmonary arterial hypertension associated with congenital heart disease. |
| PubMedID- 23052666 | This study enrolled 29 congenital heart disease cases with pulmonary arterial hypertension and 40 healthy subjects followed at our center. |
| PubMedID- 20637015 | Impact of sildenafil therapy on pulmonary arterial hypertension in adults with congenital heart disease. |
| PubMedID- 25006452 | Standardization of the diagnostic routine for children with congenital heart disease associated with pulmonary arterial hypertension (pah-chd) is crucial, in particular since inappropriate assignment to repair of the cardiac lesions (e.g., surgical repair in patients with elevated pulmonary vascular resistance) may be detrimental and associated with poor outcomes. |
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