eRAM
encyclopedia of Rare Disease Annotation for Precision Medicine
| Disease | portal hypertension |
| Comorbidity | C0020538|hypertension |
| Sentences | 7 |
| PubMedID- 20677289 | Pulmonary arterial hypertension (pah) associated with portal hypertension [portopulmonary hypertension (pphtn)] occurs in 2% to 10% of patients with advanced liver disease and carries a very poor prognosis without treatment. |
| PubMedID- 23982562 | This review summarizes the clinicopathologic features, diagnostic criteria, as well as the latest concepts in the pathogenesis and management of poph, which is defined as is a form of pulmonary arterial hypertension (pah) associated with portal hypertension with or without underlying chronic liver disease. |
| PubMedID- 19766269 | Children with congenital portosystemic venous shunt (psvs) are at risk for developing pulmonary hypertension, irrespective of the severity of portal hypertension or liver damage. |
| PubMedID- 21828952 | Pulmonary arterial hypertension (pah) in patients with portal hypertension is also referred to as portopulmonary hypertension (pphtn). |
| PubMedID- 25653708 | Hepatopulmonary syndrome (hps) and portopulmonary hypertension (pphtn) are complications of portal hypertension and cirrhosis. |
| PubMedID- 24046802 | We report a case of acute right heart pressure overload after surgical correction of the suprahepatic inferior vena cava anastomotic stricture in a 54-year-old woman who had preexisting pulmonary arterial hypertension associated with portal hypertension after orthotopic liver transplantation. |
| PubMedID- 26029592 | Poph is defined as pulmonary arterial hypertension with portal hypertension in the absence of other causes of pulmonary arterial hypertension. |
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