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eRAM

encyclopedia of Rare Disease Annotation for Precision Medicine




Disease panencephalitis, subacute sclerosing
Comorbidity C0038522|subacute sclerosing panencephalitis
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PubMedID- 25802788 subacute sclerosing panencephalitis is a progressive, fatal neurodegenerative disease caused by an aberrant measles virus in the central nervous system [1].
PubMedID- 24339595 subacute sclerosing panencephalitis (sspe) is a rare progressive demyelinating disease of the central nervous system associated with a chronic infection of brain tissue with measles virus, most commonly seen in children and young adults.
PubMedID- 22412996 Neuroborreliosis, neurosyphilis, subacute sclerosing panencephalitis, and multiple sclerosis are all characterized by cns accumulation of b-lymphocyte lineage cells such as antibody secreting cells (asc) and elevated immunoglobulin in cerebral spinal fluid [16], [17].

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