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eRAM

encyclopedia of Rare Disease Annotation for Precision Medicine




Disease neuromyelitis optica
Comorbidity C0042384|vasculitis
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PubMedID- 26582039 The differential diagnosis should include bickerstaff’s brainstem encephalitis, cns vasculitis (primary angiitis of the cns), neuromyelitis optica, sjögren’s syndrome with cns involvement, cns lymphoma, and glioma (especially when atypical clinical or mri findings are encountered), or when resistance to corticosteroid treatment occurs [4].

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