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eRAM

encyclopedia of Rare Disease Annotation for Precision Medicine




Disease macrophage activation syndrome
Comorbidity C0018203|chronic granulomatous disease
Sentences 2
PubMedID- 22119934 We describe two patients with chronic granulomatous disease (cgd) complicated by macrophage activation syndrome (mas) (secondary hemophagocytic lymphohistiocytosis) treated with intravenous immunoglobulin (ivig).
PubMedID- 23652865 A case of macrophage activation syndrome developing in a patient with chronic granulomatous disease-associated colitis.

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