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eRAM

encyclopedia of Rare Disease Annotation for Precision Medicine




Disease lupus erythematosus
Comorbidity C0001815|myelofibrosis
Sentences 3
PubMedID- 25643819 A rare combination: chylous polyserositis and autoimmune myelofibrosis as a presentation of systemic lupus erythematosus.
PubMedID- 24478609 The main reason for splenectomy was trauma(13 cases), followed by hodgkin's lymphoma (eight cases), itp (six cases),hemolyticanemia (five cases), injury in abdominal surgery (four cases),chroniclymphocytic leukemia, chronic granulomatous disease and myelofibrosis withthrombocytopenia associated with systemic lupus erythematosus (one case each).
PubMedID- 20007816 We describe a 44-year-old woman who suffered bone lytic lesions with extramedullary haematopoiesis in the setting of myelofibrosis associated with systemic lupus erythematosus.

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