eRAM
encyclopedia of Rare Disease Annotation for Precision Medicine
| Disease | biliary cirrhosis, primary, 1 |
| Comorbidity | C0008370|cholestasis |
| Sentences | 6 |
| PubMedID- 25688837 | Our findings suggest that bile canalicular lumen expansion might explain the presence of cholestasis in patients with primary biliary cirrhosis and primary sclerosing cholangitis. |
| PubMedID- 24147052 | Naic is distinguished from established ribosomopathies in that it has a single and unique clinical manifestation (cholestasis leading to biliary cirrhosis). |
| PubMedID- 20435377 | The process of chronic cholestasis eventually leads to biliary cirrhosis. |
| PubMedID- 24318962 | Finally, secondary biliary cirrhosis owing to cholestasis caused by a stricture of the hepaticojejunostomy is the most frequent indication of lt for bdi after cholecystectomy29. |
| PubMedID- 22933985 | Pbc is a female-dominant disease usually presenting intrahepatic bile duct destruction, cholestasis and fibrosis with or without chronic nonsuppurative destructive cholangitis. |
| PubMedID- 23304557 | Biliary atresia is a rare neonatal disease of unknown etiology, where obstruction of the biliary tree causes severe cholestasis, leading to biliary cirrhosis and death in the first years of life, if the condition is left untreated. |
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