eRAM
encyclopedia of Rare Disease Annotation for Precision Medicine
| Disease | idiopathic pulmonary fibrosis |
| Symptom | C1800706|usual interstitial pneumonia |
| Sentences | 1 |
| PubMedID- 24368713 | The diffuse idiopathic interstitial pneumonias describe a spectrum of parenchymal lung diseases sharing clinical, physiological, radiological and pathological similarities, including varying degrees of fibrosis, inflammation and vascular injury.1 idiopathic pulmonary fibrosis (ipf) is associated with usual interstitial pneumonia (uip), poor survival and limited treatment options.2 interstitial lung disease (ild), most typically presenting as non-specific interstitial pneumonitis, is a leading cause of death in systemic sclerosis (ssc)3 and a prominent clinical feature of other connective tissue diseases (ctds), including idiopathic inflammatory myopathy (iim) and sjögren syndrome. |
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