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eRAM

encyclopedia of Rare Disease Annotation for Precision Medicine




Disease chronic myeloproliferative disease
Symptom C0018952|extramedullary hematopoiesis
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PubMedID- 22958626 Idiopathic myelofibrosis is a rare chronic myeloproliferative disease leading to extramedullary hematopoiesis (myeloid metaplasia) with splenomegaly.

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