eRAM
encyclopedia of Rare Disease Annotation for Precision Medicine
| Disease | rosai-dorfman disease |
| Symptom | |lymphadenopathy |
| Sentences | 105 |
| PubMedID- 21743180 | Rosai dorfman disease (rdd), also known as sinus histiocytosis with massive lymphadenopathy, is a benign histiocytic proliferative disorder mainly affecting the lymph nodes. |
| PubMedID- 21906971 | Rosai and dorfman first described sinus histiocytosis with massive lymphadenopathy (shml) in 1969 with an article detailing 4 cases in which they differentiated this disease entity from the grouping of diseases categorized as histiocytosis x, where it was previously classified. |
| PubMedID- 22389884 | Sinus histiocytosis with massive lymphadenopathy (shml), also known as rosai-dorfman disease 1, is a rare pathological condition characterized by fever and lymph node enlargement. |
| PubMedID- 22973396 | Sinus histiocytosis with massive lymphadenopathy (shml), also known as rosai-dorfman disease (rdd), was first described by rosai and dorfman in 1969.1 it is a rare idiopathic proliferative disorder that is commonly characterized by painless, massive cervical lymphadenopathy. |
| PubMedID- 23267385 | In 1969, rosai-dorfman disease first reported by juan rosai and ronald dorfman as sinus histiocytosis with massive lymphadenopathy in young black male. |
| PubMedID- 25088489 | Sinus histiocytosis with massive lymphadenopathy also known as rosai-dorfman disease is a rare, benign, histiocytic disorder of unknown origin characterized by lymphadenopathy. |
| PubMedID- 24901405 | We report a unique case of rosai-dorfman disease (sinus histiocytosis with massive lymphadenopathy) involving the uterus. |
| PubMedID- 19819734 | Sinus histiocytosis with massive lymphadenopathy (rosai-dorfman disease) is a rare disease that typically occurs in lymph nodes. |
| PubMedID- 22438629 | rosai-dorfman disease (rdd), also known as sinus histiocytosis with massive lymphadenopathy is a rare disease involving the lymph nodes. |
| PubMedID- 23090417 | Background: rosai-dorfman disease (rdd), also known as sinus histiocytosis with massive lymphadenopathy, is a rare non-malignant proliferation of histiocytes of unknown aetiology. |
| PubMedID- 20418084 | Introduction: rosai-dorfman disease (rdd), also known as sinus histiocytosis with massive lymphadenopathy (shml), is a rare monocyte/macrophage proliferative disorder of varied biological behavior. |
| PubMedID- 24758864 | Background: adrenal gland involvement is a very rare extranodal presentation of sinus histiocytosis with massive lymphadenopathy (rosai-dorfman disease). |
| PubMedID- 24611075 | rosai-dorfman disease (rdd) is also known as sinus histiocytosis with massive lymphadenopathy (shml). |
| PubMedID- 22224025 | Rdd (sinus histiocytosis with massive lymphadenopathy) is characterized by massive painless bilateral lymph node enlargement in the neck. |
| PubMedID- 22083607 | Background: sinus histiocytosis with massive lymphadenopathy or rosai-dorfman disease (rdd) is a rare benign disease with nodal and extranodal involvement. |
| PubMedID- 23785592 | Sinus histiocytosis with massive lymphadenopathy, also known as rosai-dorfman disease, is a very rare inflammatory entity. |
| PubMedID- 23863552 | rosai-dorfman disease, also known as sinus histiocytosis with massive lymphadenopathy, is a benign proliferative disorder of histiocytes with an unknown etiology. |
| PubMedID- 25686890 | Background: sinus histiocytosis (rosai-dorfman disease) with massive lymphadenopathy is a rare nonneoplastic and nonlangerhans cell proliferation disorder of the histiocytes. |
| PubMedID- 20227012 | rosai-dorfman disease (also known as sinus histiocytosis with massive lymphadenopathy) is an uncommon, idiopathic, benign histiocytic lesion. |
| PubMedID- 24164002 | Rosai-dorfminan disease (rdd), or sinus histiocytosis with massive lymphadenopathy, is a benign idiopathic proliferative disorder of the histiocyte. |
| PubMedID- 21331166 | sinus histiocytosis with massive lymphadenopathy (shml) involves primarily the cervical nodes, but its histiocytes are morphologically quite different from those of lch. |
| PubMedID- 26527559 | According to the histiocytosis classification, ecd is one kind of non-langerhans cell histiocytosis, and it should be differentiated from langerhans cell histiocytosis (lch) or sinus histiocytosis with massive lymphadenopathy (shml), also known as rosai-dorfman disease (rdd). |
| PubMedID- 22110893 | Hhv-6 late antigens have also been identified in cases of rosai dorfman disease, otherwise known as sinus histiocytosis with massive lymphadenopathy, a benign chronic disease, mainly affecting children and young adults and with no progression to lymphoma. |
| PubMedID- 22028755 | The first report of sinus histiocytosis with massive lymphadenopathy (shml) was described in 1959, by destombes as a lipid storage disorder developing after inflammation.4. |
| PubMedID- 21475597 | Sinus histiocytosis with massive lymphadenopathy (shml) or rosai-dorfman disease (rdd) was first described as a distinct clinicopathological entity by rosai and dorfman in 1969. |
| PubMedID- 20351578 | Sinus histiocytosis with massive lymphadenopathy, also known as rosai-dorfman disease, is a rare entity predominantly affecting children and young adults, characterized in 95% of patients by painless bilateral cervical limphadenopathy. |
| PubMedID- 20631502 | Sinus histiocytosis with massive lymphadenopathy or rosai-dorfman disease is a rare clinicopathological entity that typically affects young adults, with patients presenting frequently with fever and painless cervical adenopathy. |
| PubMedID- 21762247 | rosai-dorfman disease (also called sinus histiocytosis with massive lymphadenopathy) involves lymph nodes or lymph nodes with extranodal sites. |
| PubMedID- 25812620 | Rosai--dorfman disease (rdd) or sinus histiocytosis with massive lymphadenopathy (shml) is a rare, benign and self--limiting disorder of unknown etiology. |
| PubMedID- 24061526 | This report describes 2 new cases of testicular involvement by rosai-dorfman disease, also known as sinus histiocytosis with massive lymphadenopathy, and reviews the clinical and pathologic features of the other cases documented in the literature (4 cases) or included in the sinus histiocytosis with massive lymphadenopathy registry (7 cases). |
| PubMedID- 25281034 | Extranodal sinus histiocytosis with massive lymphadenopathy (rosai-dorfman disease) is a non-neoplastic condition that has rarely been reported to involve the central nervous system. |
| PubMedID- 26391332 | Sinus histiocytosis with massive lymphadenopathy, or rosai-dorfman disease (rdd), is commonly characterized by painless cervical lymphadenopathy. |
| PubMedID- 26288524 | Sinus histiocytosis with massive lymphadenopathy (shml) or rosai-dorfman disease is a non-neoplastic condition which typically presents as massive, bilateral cervical lymphadenopathy and can involve multiple extranodal organ systems such as skin, eyes, and upper respiratory tract in about 28% cases. |
| PubMedID- 24864019 | Background: rosai-dorfman disease (rdd), otherwise known as sinus histiocytosis with massive lymphadenopathy (shml), usually affects young adults and commonly presents with massive painless cervical lymphadenopathy. |
| PubMedID- 21743179 | Sinus histiocytosis with massive lymphadenopathy or rosai-dorfman disease is a rare, but well documented entity. |
| PubMedID- 24758863 | rosai-dorfman disease, known as well as sinus histiocytosis with massive lymphadenopathy, is a histiocytic proliferative disorder which may affect, with an extranodal presentation, the central nervous system, in 5 % of cases with exceptional reports of simultaneous development of spinal and cranial tumors. |
| PubMedID- 26452062 | Successful treatment of recurrent autoimmune cytopenias in the context of sinus histiocytosis with massive lymphadenopathy using sirolimus. |
| PubMedID- 25346769 | Sinus histiocytosis with massive lymphadenopathy known as rosai-dorfman disease is characterized by painless bilateral cervical lymphadenopathy. |
| PubMedID- 24332663 | Rosai dorfman disease (rd), also known as sinus histiocytosis with massive lymphadenopathy (shml), is a benign histiocytic proliferative condition of unsubstantiated etiology that most often presents as bilateral painless cervical lymphadenopathy. |
| PubMedID- 20679880 | Sinus histiocytosis with massive lymphadenopathy or rosai-dorfman disease (rdd) is a rare histiocytic proliferative disorder of unknown etiology. |
| PubMedID- 26509029 | Rdd (rosai dorfman disease), also called shml (sinus histiocytosis with massive lymphadenopathy), was first described by rosai and dorfman in 1969 1. rdd is a rare and self-limiting disorder that more frequently affects children, adolescents, and young men; however, it can occur in adults and the elderly 2. its main clinical manifestation is painless cervical lymph node involvement, but other lymph nodes can also be involved. |
| PubMedID- 24587931 | Here we report a case in a 6-year-old boy of differential diagnoses including dermatopathic lymphadenitis (dl), parasitic infection, kimura's disease, hypersensitivity reactions, cat-scratch disease, sinus histiocytosis with massive lymphadenopathy (shml), hyperplasic lymph nodes, and lymphoma. |
| PubMedID- 26073916 | Introduction: rosai-dorfman disease (rdd), also known as sinus histiocytosis with massive lymphadenopathy, is a rare histiocytic disorder of unclear etiology. |
| PubMedID- 23252252 | The paper describes a case of diffuse large b-cell lymphoma detected in a patient 13 months after sinus histiocytosis with massive lymphadenopathy (shml) or rosai-dorfman disease (rdd) being diagnosed together with active hepatitis b virus infection. |
| PubMedID- 23510963 | rosai-dorfman disease, formerly known as 'sinus histiocytosis with massive lymphadenopathy', is a rare self-limiting histiocytic proliferative disorder typically presenting early in life with cervical lymphadenopathy and nonspecific systemic symptoms. |
| PubMedID- 25401088 | rosai-dorfman disease (rdd) is a proliferative histiocytic disorder of unknown etiology, which is characterized by sinus histiocytosis with massive lymphadenopathy (1). |
| PubMedID- 22279491 | they include dendritic cell related disorders such as langerhans cell histiocytosis (lch) and macrophage related disorders, also known as the non-langerhans cell histiocytoses (non-lch), which include the hemophagocytic syndromes, sinus histiocytosis with massive lymphadenopathy (shml or rosai-dorfman disease) and erdheim–chester disease (ecd). |
| PubMedID- 24707426 | The disease was first described by destombes in 1965 and later, in 1969, rosai-dorfman disease was first reported by juan rosai and roland dorfman as sinus histiocytosis with massive lymphadenopathy in young black males. |
| PubMedID- 24626670 | Rdd was first described by rosai and dorfman in 1969 as sinus histiocytosis with massivelymphadenopathy.1 classically,it presents as bilateral painless cervical and paratracheal lymphadenopathy, which canbe massive, in 90% of the cases. |
| PubMedID- 21630484 | rosai-dorfman disease (rdd) or sinus histiocytosis with massive lymphadenopathy (shml) is a rare disorder typically manifesting as enlarged lymph nodes with or without systemic involvement. |