PedAM

Pediatric Disease Annotations & Medicines

Disease	pulmonary fibrosis
Phenotype	C0020538\|hypertension
Sentences	21
PubMedID- 21660584	Prevalence of pulmonary hypertension in patients with idiopathic pulmonary fibrosis: correlation with physiological parameters.
PubMedID- 25055292	Conclusion: the relative ct volume of any single lesion was of limited value in predicting pulmonary hypertension in patients with pulmonary fibrosis and emphysema.
PubMedID- 26099567	As progressive pulmonary fibrosis can lead to pulmonary hypertension (rockey et al., 2015), it will be of considerable interest to ask whether endmt participates in the regulatory network of human ph and, if so, what is the exact role of endmt in the development of ph?
PubMedID- 25435929	pulmonary fibrosis may then lead to pulmonary hypertension and right-sided heart failure, the latter of which is the leading cause of mortality in patients with systemic sclerosis.
PubMedID- 19643948	Pulmonary hypertension in patients with combined pulmonary fibrosis and emphysema syndrome.
PubMedID- 24918967	Rationale: the development of pulmonary hypertension (ph) in patients with idiopathic pulmonary fibrosis (ipf) or chronic obstructive pulmonary disease (copd) is associated with increased morbidity.
PubMedID- 26113671	Furthermore, chymase inhibition prevented big endothelin-1-induced vasoconstriction of the pulmonary arteries.therefore, chymase plays a role in the pathogenesis of pulmonary hypertension associated with pulmonary fibrosis and may represent a promising therapeutic target.
PubMedID- 20946337	Heart rate recovery after six-minute walk test predicts pulmonary hypertension in patients with idiopathic pulmonary fibrosis.
PubMedID- 21835902	Background: pulmonary hypertension (ph) associated with pulmonary fibrosis (pf) is a severe condition with poor outcome.
PubMedID- 23734851	Clinical case: combined pulmonary fibrosis and emphysema with pulmonary hypertension--clinical management.
PubMedID- 25444371	Effect of pulmonary hypertension on survival in patients with idiopathic pulmonary fibrosis after lung transplantation: an analysis of the united network of organ sharing registry.
PubMedID- 23840349	Pulmonary hypertension in patients with idiopathic pulmonary fibrosis - the predictive value of exercise capacity and gas exchange efficiency.
PubMedID- 26029570	This report describes a case of successful treatment with bosentan for severe pulmonary hypertension in a patient with idiopathic pulmonary fibrosis.
PubMedID- 25836609	Incidence and clinical characteristics of pulmonary hypertension in patients with idiopathic pulmonary fibrosis.
PubMedID- 22428220	Failure of noninvasive prediction of pulmonary hypertension in patients with idiopathic pulmonary fibrosis.
PubMedID- 20639137	The development of pulmonary arterial hypertension (pah) in patients with pulmonary fibrosis is well recognized.
PubMedID- 26319484	Influence of pulmonary hypertension on patients with idiopathic pulmonary fibrosis awaiting lung transplantation.
PubMedID- 23928001	Pulmonary hypertension (ph) associated with pulmonary fibrosis (pf) considerably worsens prognosis of interstitial lung diseases (ild).
PubMedID- 20130830	Sildenafil-induced preferential vasodilation was observed in patients with pulmonary hypertension due to chronic pulmonary fibrosis and hence chronic hypoxia [23].
PubMedID- 23372927	The degree of pressure overload is usually mild when pulmonary hypertension develops in patients with idiopathic pulmonary fibrosis, and angioproliferative lesions are rarely seen in these patients.
PubMedID- 22054725	We describe a 76-year-old former smoker with a diagnosis of combined pulmonary fibrosis and emphysema associated with pulmonary hypertension and rapidly progressive right heart failure, in whom combined treatment with sitaxsentan and sildenafil resulted in sustained improvement of his clinical condition and exercise performance, without any relevant adverse events.

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