PedAM
Pediatric Disease Annotations & Medicines
| Disease | pulmonary fibrosis |
| Phenotype | C0010674|cystic fibrosis |
| Sentences | 2 |
| PubMedID- 20827647 | In end-stage cystic fibrosis and patients with idiopathic pulmonary fibrosis, alternative treatment options are currently not available and lung transplantation is indicated. |
| PubMedID- 23523785 | This data identifies ceramide as a key molecule associated with pulmonary fibrosis in cystic fibrosis mice and demonstrate for the first time that prolonged inhibition of acid sphingomyelinase is able to attenuate fibrosis and inflammation in this animal model. |
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