PedAM

Pediatric Disease Annotations & Medicines

Disease	n syndrome
Phenotype	C0023890\|cirrhosis
Sentences	7
PubMedID- 23789457	[congenital bile duct hypoplasia (alagille-watson syndrome)--a rare cause of biliary cirrhosis in adults].
PubMedID- 21606920	The experimental study of liver cirrhosis with portal hypertension syndrome, modeled in 38 dogs, has been performed.
PubMedID- 24790454	The clinical course of the disease is characterized by a “compensated” or asymptomatic phase followed by a rapidly progressive phase “decompensated”, resulting in development of complications (jaundice, variceal hemorrhage, ascites, encephalopathy) secondary to the two main syndromes associated with cirrhosis, ie, portal hypertension and hepatic insufficiency.2,3 therefore, cirrhosis is classified into four stages, ie, two compensated stages (absence of ascites or presence of nonhemorrhagic esophageal varices) and two decompensated stages (presence of ascites and variceal bleeding), which are related to hemodynamic changes in terms of portal pressure gradient and histological stages of fibrosis.2,4 recently, a fifth stage has been proposed, that consists of infection (sepsis) in critically ill patients, and its presence has been associated with increased mortality5 (figure 1).
PubMedID- 24423911	Objective: to explore the clinical characteristics of primary biliary cirrhosis (pbc) with sjogren syndrome (ss) so as to seek diagnostic rationales.
PubMedID- 25280538	Methods: we collected the leukocyte samples of three hepatitis b-caused cirrhosis (hbc) patients with dampness-heat accumulation syndrome (dhas) and three hbc patients with liver depression and spleen deficiency syndrome (ldsds) for microarray analysis.
PubMedID- 22245374	Steatohepatitis and liver cirrhosis in chanarin-dorfman syndrome with a new abdh5 mutation.
PubMedID- 21094870	A 27-year-old japanese man underwent liver transplantation because of uncompensated cirrhosis due to dorfman-chanarin syndrome (dcs).

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