PedAM
Pediatric Disease Annotations & Medicines
| Disease | heart disease |
| Phenotype | C1619734|pulmonary arterial hypertension |
| Sentences | 65 |
| PubMedID- 20549685 | pulmonary arterial hypertension associated with congenital heart disease (apah-chd) (n = 61, 34%) was more common than idiopathic pah (ipah) (n = 36, 20%). |
| PubMedID- 24176071 | Uncorrected congenital heart disease (chd) frequently leads to pulmonary arterial hypertension (pah), the most severe form of which is eisenmenger syndrome (es). |
| PubMedID- 20728407 | Endothelin receptor antagonists are an effective long term treatment option in pulmonary arterial hypertension associated with congenital heart disease with or without trisomy 21. |
| PubMedID- 22068906 | Plasma von willebrand factor as a predictor of survival in pulmonary arterial hypertension associated with congenital heart disease. |
| PubMedID- 20856682 | Adult patients with pulmonary arterial hypertension due to congenital heart disease: a review on advanced medical treatment with bosentan. |
| PubMedID- 24081196 | Objectives: the treatment of choice for congenital heart disease (chd) with pulmonary arterial hypertension (pah) is still controversial. |
| PubMedID- 23962785 | Background: eisenmenger syndrome (es) represents the extreme manifestation of pulmonary arterial hypertension in patients with congenital heart disease, associated with significant exercise intolerance and mortality. |
| PubMedID- 23064558 | Objective: to compare the acute hemodynamic effects of aerosolized iloprost and inhaled nitric oxide (no) in adult congenital heart disease (chd) patients with severe pulmonary arterial hypertension (pah). |
| PubMedID- 26413109 | Background and objectives: despite remarkable advances in pediatric cardiology, pulmonary arterial hypertension associated with congenital heart disease remains a major problem. |
| PubMedID- 25620261 | [management of pulmonary arterial hypertension associated with congenital heart disease with specific pulmonary arterial hypertension vasoactive drugs combined with transcatheter closure strategy:a case report]. |
| PubMedID- 25911012 | Decrease in quality of life predicts mortality in adult patients with pulmonary arterial hypertension due to congenital heart disease. |
| PubMedID- 23041100 | Efficacy of exercise training in pulmonary arterial hypertension associated with congenital heart disease. |
| PubMedID- 23241414 | Objective: pulmonary arterial hypertension due to congenital heart disease (chd-pah) has a poor prognosis. |
| PubMedID- 26135803 | Riociguat for pulmonary arterial hypertension associated with congenital heart disease. |
| PubMedID- 23052666 | This study enrolled 29 congenital heart disease cases with pulmonary arterial hypertension and 40 healthy subjects followed at our center. |
| PubMedID- 24942698 | pulmonary arterial hypertension (pah) associated with congenital heart disease (pah-chd) is a common late complication, and is associated with increased morbidity and mortality. |
| PubMedID- 25650280 | The progressive rise in pulmonary vascular resistance and increased pressures in the right heart provocated reversal of the shunt may arise with the development of eisenmenger' syndrome the most advanced form de pulmonary arterial hypertension associated with congenital heart disease. |
| PubMedID- 21763017 | Introduction: pulmonary arterial hypertension (pah) in patients with congenital heart disease (chd) usually has a homogeneous pressure distribution. |
| PubMedID- 25787791 | pulmonary arterial hypertension associated with congenital heart disease. |
| PubMedID- 24577356 | Right ventricular diastolic performance in children with pulmonary arterial hypertension associated with congenital heart disease: correlation of echocardiographic parameters with invasive reference standards by high-fidelity micromanometer catheter. |
| PubMedID- 23720182 | [pulmonary arterial hypertension in patients with congenital heart disease: current issues and health care situation]. |
| PubMedID- 24814894 | Blood biomarkers and their potential role in pulmonary arterial hypertension associated with congenital heart disease. |
| PubMedID- 25008885 | Objective: to observe the clinical efficacy and safety of sildenafil in the treatment of high altitude heart disease associated with severe pulmonary arterial hypertension (pah) in children. |
| PubMedID- 23351920 | However, its long-term efficacy and safety in patients with pulmonary arterial hypertension (pah) associated with complex congenital heart disease (chd) is unknown. |
| PubMedID- 25604592 | pulmonary arterial hypertension associated with congenital heart disease and eisenmenger syndrome: current practice in pediatrics. |
| PubMedID- 23895034 | The challenge of managing pulmonary arterial hypertension in adults with congenital heart disease. |
| PubMedID- 22781765 | [screening study of pulmonary arterial hypertension in patients with congenital heart diseases]. |
| PubMedID- 24093869 | Value of systolic right ventricular function parameters in children with pulmonary arterial hypertension associated with congenital heart diseases. |
| PubMedID- 24629043 | Apah-chd: pulmonary arterial hypertension associated with congenital heart disease; apah-ctd: pulmonary arterial hypertension associated with connective tissue disease; ci: confidence interval; hr: hazard ratio; mpap: mean pulmonary arterial pressure; nyha: new york heart association; pah: pulmonary arterial hypertension; pcwp: pulmonary capillary wedge pressure; rhc: right heart catheterization; sd: standard deviation; 6mwd: 6-minute walk distance. |
| PubMedID- 25737007 | This study investigated the clinical value of plasma asymmetrical dimethyl-l-arginine (adma) level in the diagnosis, staging, and treatment response in congenital heart disease (chd) patients with pulmonary arterial hypertension (pah). |
| PubMedID- 22257586 | However, it is particularly useful in patient with pulmonary arterial hypertension associated with congenital heart disease. |
| PubMedID- 23236330 | Eisenmenger syndrome is the clinical phenotype of an extreme form of pulmonary arterial hypertension associated with congenital heart disease. |
| PubMedID- 22081363 | Recent progress in treatment of pulmonary arterial hypertension due to congenital heart disease. |
| PubMedID- 21093377 | A review of the management of pulmonary arterial hypertension associated with congenital heart disease. |
| PubMedID- 25549894 | Eisenmenger's syndrome (es) is the most advanced form of pulmonary arterial hypertension (pah) associated with congenital heart diseases (chd). |
| PubMedID- 25847058 | Methods: using micrornas microarray, we profiled the micrornas in the lung specimen from 12 congenital heart disease patients, (6 with pulmonary arterial hypertension and the others without). |
| PubMedID- 25443244 | pulmonary arterial hypertension associated with congenital heart disease: recent advances and future directions. |
| PubMedID- 21371683 | Ambrisentan for pulmonary arterial hypertension due to congenital heart disease. |
| PubMedID- 23280192 | Objective: the aim of this study is to determine the relationship between the cardiac catheterization findings and pulsed-wave (pw) doppler and doppler tissue imaging (dti) in pulmonary arterial hypertension patients with congenital heart disease with intracardiac shunts. |
| PubMedID- 20026774 | Background: advanced therapy (at) for pulmonary arterial hypertension in the context of congenital heart disease (eisenmenger syndrome) improves pulmonary hemodynamics, functional class, and the 6-minute walk test. |
| PubMedID- 24790070 | C-reactive protein in adults with pulmonary arterial hypertension associated with congenital heart disease and its prognostic value. |
| PubMedID- 23640439 | Accuracy of doppler echocardiography in the assessment of pulmonary arterial hypertension in patients with congenital heart disease. |
| PubMedID- 24571873 | Background: congenital heart disease with severe pulmonary arterial hypertension (spah), previously thought to have irreversible pulmonary vascular disease (pvd), has been recently successfully corrected using diagnostic treatment and repair strategy by our surgery team. |
| PubMedID- 25076993 | Saudi guidelines on the diagnosis and treatment of pulmonary hypertension: pulmonary arterial hypertension associated with congenital heart disease. |
| PubMedID- 21723630 | Prolonged beneficial effect of bosentan treatment and 4-year survival rates in adult patients with pulmonary arterial hypertension associated with congenital heart disease. |
| PubMedID- 21943933 | Efficacy and safety of bosentan for pulmonary arterial hypertension in adults with congenital heart disease. |
| PubMedID- 25006452 | Standardization of the diagnostic routine for children with congenital heart disease associated with pulmonary arterial hypertension (pah-chd) is crucial, in particular since inappropriate assignment to repair of the cardiac lesions (e.g., surgical repair in patients with elevated pulmonary vascular resistance) may be detrimental and associated with poor outcomes. |
| PubMedID- 23548773 | We explored the hypothesis that the level of ace2 protein contents may be decreased in patients with pulmonary arterial hypertension (pah) due to congenital heart disease (chd). |
| PubMedID- 26459910 | We validated our methods by quantifying mirna expression profiles in the sera of the patients with pulmonary arterial hypertension associated with congenital heart disease. |
| PubMedID- 22086272 | Advanced therapy for pulmonary arterial hypertension due to congenital heart disease: a clinical perspective in a new therapeutic era. |
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