PedAM
Pediatric Disease Annotations & Medicines
| Disease | congenital hepatic fibrosis |
| Symptom | C0020541|portal hypertension |
| Sentences | 3 |
| PubMedID- 22541062 | Liver disease in ciliopathies may be a congenital hepatic fibrosis, with risks of portal hypertension and cholangitis, or a more variable biliary disease. |
| PubMedID- 25113295 | Most notably, arpkd patients have congenital hepatic fibrosis, which can lead to portal hypertension, requiring close follow-up by pediatric gastroenterologists. |
| PubMedID- 22736301 | portal hypertension due to congenital hepatic fibrosis leading to splenomegaly and varices can be the presenting feature. |
Page: 1