PedAM
Pediatric Disease Annotations & Medicines
| subcutaneous panniculitis-like t-cell lymphoma | ||||
| Disease ID | 1417 |
|---|---|
| Disease | subcutaneous panniculitis-like t-cell lymphoma |
| Definition | A cytotoxic primary cutaneous T-cell lymphoma. Recent studies suggest there are at least two groups of subcutaneous panniculitis-like T-cell lymphomas, each with distinct histologic features, immunophenotypic profile, and prognosis. One group has an alpha/beta, CD8 positive phenotype, involves only subcutaneous tissues, and usually has an indolent clinical course. The second group has a gamma/delta phenotype, is CD8 negative, often co-expresses CD56, is not confined to the subcutaneous tissues, and usually has a poor prognosis. In the recent WHO-EORTC classification, the term subcutaneous panniculitis-like T-cell lymphoma is reserved for cases with an alpha/beta, CD8 positive phenotype. Cases with a gamma/delta phenotype are included in the group of cutaneous gamma/delta T-cell lymphomas. |
| Synonym | sptcl subcutaneous panniculitic cutaneous t-cell lymphoma subcutaneous panniculitic cutaneous t-cell lymphoma (disorder) subcutaneous panniculitic t-cell lymphoma subcutaneous panniculitic t-cell lymphoma (morphologic abnormality) subcutaneous panniculitis-like t-cell lymphoma (alpha/beta type) subcutaneous panniculitis-like t-cell lymphoma, alpha/beta type |
| Orphanet | |
| ICD10 | |
| UMLS | C0522624 |
| SNOMED-CT | |
| Comorbidity | UMLS | Disease | Sentences' Count(Total Sentences:4) |
| Curated Gene | (Waiting for update.) |
| Inferring Gene | (Waiting for update.) |
| Text Mined Gene | (Waiting for update.) |
| Locus | (Waiting for update.) |
| Disease ID | 1417 |
|---|---|
| Disease | subcutaneous panniculitis-like t-cell lymphoma |
| Integrated Phenotype | (Waiting for update.) |
| Text Mined Phenotype | HPO | Name | Sentences' Count(Total Phenotypes:4) |
| Disease ID | 1417 |
|---|---|
| Disease | subcutaneous panniculitis-like t-cell lymphoma |
| Manually Symptom | UMLS | Name(Total Manually Symptoms:1) C2364133 | infection |
| Text Mined Symptom | (Waiting for update.) |
Manually Genotype(Total Text Mining Genotypes:0) |
|---|
| (Waiting for update.) |
All Snps(Total Genotypes:0) | |
|---|---|
| (Waiting for update.) | |
GWASdb Annotation(Total Genotypes:0) | |
|---|---|
| (Waiting for update.) | |
GWASdb Snp Trait(Total Genotypes:0) | |
|---|---|
| (Waiting for update.) | |
Mapped by lexical matching(Total Items:0) |
|---|
| (Waiting for update.) |
Mapped by homologous gene(Total Items:0) |
|---|
| (Waiting for update.) |
Chemical(Total Drugs:0) | |
|---|---|
| (Waiting for update.) | |
FDA approved drug and dosage information(Total Drugs:0) | |
|---|---|
| (Waiting for update.) | |
FDA labeling changes(Total Drugs:0) | |
|---|---|
| (Waiting for update.) | |